2022 ARC/EULAR 诊断和管理自身炎症I型干扰素病（CANDLE/PRAAS、SAVI和AGS）应考虑的要点

2022-03-21 美国风湿病学会 Arthritis & Rheumatology

自身炎症 I 型干扰素病、慢性非典型中性粒细胞性皮肤病伴脂肪代谢障碍和体温升高/蛋白酶体相关自身炎症综合征 (CANDLE/PRAAS)、干扰素基因刺激物 (STING) 相关的婴儿期发病血管病 (S

中文标题：

英文标题：

The 2021 European Alliance of Associations forRheumatology/American College of RheumatologyPoints to Consider for Diagnosis and Managementof Autoinflammatory Type I Interferonopathies:CANDLE/PRAAS, SAVI, and AGS

发布机构：

美国风湿病学会

发布日期：

2022-03-21

简要介绍：

自身炎症 I 型干扰素病、慢性非典型中性粒细胞性皮肤病伴脂肪代谢障碍和体温升高/蛋白酶体相关自身炎症综合征 (CANDLE/PRAAS)、干扰素基因刺激物 (STING) 相关的婴儿期发病血管病 (SAVI) 和 Aicardi-Goutières 综合征。

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